Ultrasonography of abdominal muscles: Differential diagnosis of late-onset Pompe disease and
myotonic dystrophy type 1. Front Neurol. 2022 Sep 6:13:944464. doi: 10.3389/fneur.2022.944464. eCollection 2022. Pei-Chen Hsieh, Chun-Wei Chang, Long-Sun Ro, Chin-Chang Huang, Jia-En Chi, Hung-Chou Kuo*.
Altered Metabolic Profiles of the Plasma of Patients with Amyotrophic Lateral Sclerosis.
Biomedicines. 2021 Dec 18;9(12):1944. doi: 10.3390/biomedicines9121944. Kuo-Hsuan Chang, Chia-Ni Lin, Chiung-Mei Chen, Rong-Kuo Lyu, Chun-Che Chu, Ming-Feng Liao, Chin-Chang Huang, Hong-Shiu Chang, Long-Sun Ro, Hung-Chou Kuo*.
Cross-Sectional Area Reference Values for Sonography of Peripheral Nerves in Taiwanese Adults. Front Neurol. 2021 Nov 3:12:722403. doi: 10.3389/fneur.2021.722403. eCollection 2021. Pei-Chen Hsieh, Kuo-Hsuan Chang, Yih-Ru Wu, Long-Sun Ro, Chun-Che Chu, Rong-Kuo Lyu, Ming-Feng Liao, Hung-Chou Kuo*.
Prophylactic Heme Arginate Infusion for Acute Intermittent Porphyria. Front Pharmacol. 2021 Oct 6:12:712305. doi: 10.3389/fphar.2021.712305. eCollection 2021. Hung-Chou Kuo*, Chia-Ni Lin, Yi-Fen Tang.
Profiling of Serum Metabolites of Acute Intermittent Porphyria and Asymptomatic HMBS Mutation Carriers. Cells. 2021 Sep 28;10(10):2579. doi: 10.3390/cells10102579. Chia-Ni Lin, Ming-Shi Shiao, Mei-Ling Cheng, Chiung-Mei Chen, Hung-Chou Ku*.
Reappraisal of the incidence, various types and risk factors of malignancies in patients with dermatomyositis and polymyositis in Taiwan. Sci Rep. 2021 Feb 25;11(1):4545. doi: 10.1038/s41598-021-83729-5. Jung-Lung Hsu#, Ming-Feng Liao#, Chun-Che Chu, Hung-Chou Kuo, Rong-Kuo Lyu, Hong-Shiu Chang, Chiung-Mei Chen, Yih-Ru Wu, Kuo-Hsuan Chang, Yi-Ching Weng, Chun-Wei Chang, Hsing-I Chiang, Chih-Kuang Cheng, Pai-Wei Lee, Chin-Chang Huang, Long-Sun Ro*.
Differences in Clinical Presentation of Behavioral and Psychological Symptoms of Dementia in Alzheimer's Disease According to Sex and Education Level.
J Alzheimers Dis. 2020;78(2):711-719. doi: 10.3233/JAD-200507. Kuo-Hsuan Chang, Chin-Chang Huang, Chiung-Mei Chen, Hsiu-Chuan Wu, Hung-Chou Kuo*.
Granulocyte Colony Stimulating Factor (GCSF) Can Attenuate Neuropathic Pain by Suppressing Monocyte Chemoattractant Protein-1 (MCP-1) Expression, through Upregulating the Early MicroRNA-122 Expression in the Dorsal Root Ganglia. Cells. 2020 Jul 11;9(7):1669. doi: 10.3390/cells9071669. Ming-Feng Liao, Jung-Lung Hsu, Kwok-Tung Lu, Po-Kuan Chao, Mei-Yun Cheng, Hui-Ching Hsu, Ai-Lun Lo, Yun-Lin Lee, Yu-Hui Hung, Rong-Kuo Lyu, Hung-Chou Kuo, Chun-Che Chu, Long-Sun Ro*.
Diabetic Distal Symmetrical Polyneuropathy: Correlation of Clinical, Laboratory, and Electrophysiologic Studies in Patients with Type 2 Diabetes Mellitus. J Diabetes Res. 2020 Jul 3;2020:6356459. doi: 10.1155/2020/6356459. eCollection 2020. Yi-Ching Weng, Sung-Sheng Tsai, Rong-Kuo Lyu, Chun-Che Chu, Long-Sun Ro, Ming-Feng Liao, Hong-Shiu Chang, Chiung-Mei Chen, Jawl-Shan Hwang, Hung-Chou Kuo*.
Clinical Presentations and Outcome Studies of Cranial Nerve Involvement in Herpes Zoster Infection: A Retrospective Single-Center Analysis. J Clin Med. 2020 Mar 30;9(4):946. doi: 10.3390/jcm9040946. Po-Wei Tsau, Ming-Feng Liao, Jung-Lung Hsu, Hui-Ching Hsu, Chi-Hao Peng, Yu-Ching Lin, Hung-Chou Kuo, Long-Sun Ro*.
A Hybrid Fuzzy Clustering Approach for the Recognition and Visualization of MRI Images of Parkinson's Disease. IEEE Access, Volume: 8, Page(s): 25041 - 25051. Date of Publication: 27 January 2020. DOI: 10.1109/ACCESS.2020.2969806. YO-PING HUANG*, (Fellow, IEEE), PRITPAL SINGH, HUNG-CHOU KUO*.
Sensor-based detection of abnormal events for elderly people using deep belief networks. Int. J. Ad Hoc and Ubiquitous Computing, Vol. 33, No. 1, pp.36–47. Huang YP*, Basanta H, Kuo HC, Chiao, HT.
Clinical, neuroimaging, and nerve conduction characteristics of spontaneous Conus Medullaris infarction. BMC Neurol. 2019 Dec 17;19(1):328. doi: 10.1186/s12883-019-1566-1. Weng YC, Chin SC, Wu YY, Kuo HC*.
A Fuzzy Approach to Determining Critical Factors of Diabetic Retinopathy and Enhancing Data Classification Accuracy. International Journal of Fuzzy Systems. September 2019, Volume 21, Issue 6, pp 1844-1857. Yo-Ping Huang*, Haobijam Basanta, Tzu-Hao Wang, Hung-Chou Kuo, Wei-Chi Wu.
Correlation between visual association memory test and structural changes in patients with Alzheimer's disease and amnestic mild cognitive impairment. Journal of the Formosan Medical Association. Volume 118, Issue 9, September 2019, Pages 1325-1332. https://doi.org/10.1016/j.jfma.2018.12.001. Huang KL, Hsiao IT, Kuo HC, Hsieh CJ, Hsieh YC, Wu YM, Wey SP, Yen TC, Lin KJ*, Huang CC*.
A comparison between spinal cord infarction and neuromyelitis optica spectrum disorders: Clinical and MRI studies. Sci Rep. 2019 May 15;9(1):7435. doi: 10.1038/s41598-019-43606-8. Hsu JL, Cheng MY, Liao MF, Hsu HC, Weng YC, Chang KH, Chang HS, Kuo HC, Huang CC, Lyu RK, Lin KJ, Ro LS*.
A metabolomic approach to identifying biomarkers in blood of Alzheimer's disease. Annals of Clinical and Translational Neurology.2019 Mar;6(3):537-545. https://doi.org/10.1002/acn3.726. Chia-Ni Lin, Chin-Chang Huang, Kuo-Lun Huang, Kun-Ju Lin, Tzu-Chen Yen, Hung-Chou Kuo*
Predictive Factors for Early Initiation of Artificial Feeding in Patients With Sporadic Creutzfeldt-Jakob Disease. Front. Neurol. 2018 Jul 3;9:496. doi: 10.3389/fneur.2018.00496. Hsieh PC, Li HT, Chang CW, Wu YR, Kuo HC*.
Genetic and functional characters of GRN p.T487I mutation in Taiwanese patients with atypical parkinsonian disorders. Parkinsonism Relat Disord. 2018 Jun;51:61-66. doi: 10.1016/j.parkreldis.2018.02.045. Epub 2018 Feb 28. Chang KH, Lee GC, Huang CC, Kuo HC, Chen CM, Hsiao YC, Hsu HC, Hsu KJ, Lin CH, Chang CW, Lee-Chen GJ, Wu YR*.
Validation and evaluation of two porphobilinogen deaminase activity assays for diagnosis of acute intermittent porphyria. Clin Chim Acta. 2018 Apr;479:1-6. doi: 10.1016/j.cca.2018.01.009. Epub 2018 Jan 6. Lin CN, Huang YC, Ro LS, Liao MF, Ning HC, Kuo HC*.
Elevated serum levels of endothelin-1 in patients with chronic inflammatory demyelinating polyneuropathy. Clinica Chimica Acta.2018 Jan;476:49-53. Chang CW, Wu HC, Lyu RK, Lo YS, Chen CM, Ro LS, Chang HS, Huang CC, Liao MF, Wu YR, Kuo HC, Chu CC, Weng YC, Wei PT, Lo AL, Chang KH*.
Health Symptom Checking System for Elderly People Using Fuzzy Analytic Hierarchy Process. Applied System Innovation. 2018;1(2):10.非SCI. Yo-Ping Huang*, Haobijam Basanta, Hung-Chou Kuo, Andy Huang.
A prospective, observational study of patients with uncommon distal symmetric painful small-fiber neuropathy. PLoS One. 2017 Sep 28;12(9):e0183948. doi: 10.1371/journal.pone.0183948. eCollection 2017. Hsu JL, Liao MF, Hsu HC, Weng YC, Lo AL, Chang KH, Chang HS, Kuo HC, Huang CC, Ro LS.
Dual-phase 18F-florbetapir positron emission tomography in patients with primary progressive aphasia, Alzheimer's disease, and healthy controls: A preliminary study. J Formos Med Assoc. 2017 Dec;116(12):964-972. doi: 10.1016/j.jfma.2017.03.003. Epub 2017 Apr 20. Kuo HC, Hsiao IT, Hsieh CJ, Huang CY, Huang KL, Wai YY, Chuang WL, Kung MP, Chu YC, Yen TC, Lin KJ, Huang CC*.
Phenotypic expressions of hereditary Transthyretin Ala97Ser related Amyloidosis (ATTR) in Taiwanese. BMC Neurol. 2017 Sep 7;17(1):178. doi: 10.1186/s12883-017-0957-4. Hsu HC, Liao MF, Hsu JL, Lo AL, Kuo HC, Lyu RK, Wu VC, Wang CW, Ro LS.
Disturbance of Plasma Lipid Metabolic Profile in Guillain-Barre Syndrome. Sci Rep. 2017 Aug 15;7(1):8140. doi: 10.1038/s41598-017-08338-7. Tang HY, Chiu DT, Lin JF, Huang CY, Chang KH, Lyu RK, Ro LS, Kuo HC, Cheng ML, Chen CM.
Non-alcoholic Wernicke's encephalopathy with cortical involvement and polyneuropathy following gastrectomy Metabolic Brain Disease, October 2017, Volume 32, Issue 5, pp 1649–1657. Wei-Chia Tsao, Long-Sun Ro, Chiung-Mei Chen, Hong-Chiu Chang, Hung-Chou Kuo*
Peripheral neuropathy in limbic encephalitis with anti-glutamate receptor antibodies Brain Behavior 2017 DOI: 10.1002/brb3.779. Yi-Chia Wei, Chin-Chang Huang, Chi-Hung Liu, Hung-Chou Kuo, Lin Jainn-Jim
Dual-phase 18F-florbetapir positron emission tomography in patients with primary progressive aphasia, Alzheimer's disease, and healthy controls: A preliminary study J Formos Med Assoc 2017 (SCI) (in press) https://doi.org/10.1016/j.jfma.2017.03.003. Hung-Chou Kuo, Ing-Tsung Hsiao, Chia-Ju Hsieh, Chu-Yun Huang, Kuo-Lun Huang, Yau-Yau Wai ,Wen-Li Chuang, Mei-Ping Kung, Yi-Chuan Chu, Tzu-Chen Yen, Kun-Ju Lin, Chin-Chang Huang
Correlations of clinical, neuroimaging, and electrophysiological features in Hirayama disease Medicine (Baltimore). 2016; 95(28): e4210. Ming-Feng Liao, Hong-Shiu Chang, Kuo-Hsuan Chang, Long-Sun Ro, Chun-Che Chu, Hung-Chou Kuo, Rong-Kuo Lyu
Correlations between biophysical dysfunctions and clinical phenotypes of GJB1 mutations Ann Clin Translat Neurol (ACTN) 2016; 3(11): 854–865. doi:10.1002/acn3.347. Pei-Chien Tsai, De-Ming Yang, Yi-Chu Liao, Tai-Yu Chiu, Hung-Chou Kuo, Yu-Ping Su, Yuh-Cherng Guo, Bing-Wen Soong, Kon-Ping Lin, Yo-Tsen Liu, Yi-Chung Lee
Clinical and Electrodiagnostic Characteristics of nitrous oxide-induced neuropathy in Taiwan Clin Neurophysiol 2016; 127: 3288–3293. http://dx.doi.org/10.1016/j.clinph.2016.08.005. Han-Tao Li, Chun-Che Chu, Kuo-Hsuan Chang, Ming-Feng Liao, Hong-Shiu Chang, Hung-Chou Kuo, Rong-Kuo Lyu
Porphyric neuropathies in an acute intermittent porphyria family Neuropathology 2016;36:290-294. doi:10.1111/neup.12272. Hung-Chou Kuo*, Long-Sun Ro, Shih-Ming Jung, Chin-Chang Huang, Chun-Che Chu
Reply to "Demyelinating Neuropathy in Genetically-Confirmed Acute Intermittent Porphyria" comment to The Clinical Presentation and Electrophysiological Findings of Porphyric Neuropathies" Muscle Nerve 2015; 52 (5): 917-918. DOI 10.1002/mus.24732. Hung-Chou Kuo*
Wegener's granulomatosis with nervous system involvement: a hospital-based study Eur Neurol. 2015;73(3-4):197-204. doi: 10.1159/000375492. Epub 2015 Mar 10. Yu-Hua Huang, Long-Sun Ro, Rong-Kuo Lyu, Hong-Shiu Chang, Yih-Ru Wu, Hung-Chou Kuo*
Family caregivers’ role implementation at different stages of dementia Clin Interv Aging 2015;10: 135–146. (SCI) Huei-Ling Huang, Yea-Ing L Shyu, Min-Chi Chen, Chin-Chang Huang, Hung-Chou Kuo, Sien-Tsong Chen, Wen-Chuin Hsu
High frequency of SPG4 in Taiwanese families with autosomal dominant hereditary spastic paraplegia BMC Neurology. 2014; 14:216. doi:10.1186/s12883-014-0216-x Min-Yu Lan, Yung-Yee Chang, Tu-Hseuh Yeh, Szu-Chia Lai, Chia-Wei Liou, Hung-Chou Kuo, Yih-Ru Wu, Rong-Kuo Lyu, Jen-Wen Hung, Ying-Chao Chang, Chin-Song Lu
Effect of coexistent carpal tunnel abnormality on sensory conduction findings in polyneuropathy J Clin Neuromusc Dis 2014;16:51-58. Rong-Kuo Lyu, Ming-Feng Liao, Hung-Chou Kuo, Chu-Che Chu, Kuo-Hsuan Chang
Cerebrospinal fluid biomarkers for neuropsychological symptoms in early stage of late-onset Alzheimer's disease Int J Neurosci 2015;125(10): 747-754. doi:10.3109/00207454.2014.971787. Hung-Chou Kuo*, Hsiu-Chuan Yen, Chin-Chang Huang, Wen-Chuin Hsu, Hsing-Ju Wei, Chih-Lung Lin
The clinical presentation and electrophysiological findings of porphyric neuropathies: a follow-up study Muscle Nerve 2015;51:363-369. doi: 10.1002/mus.24327. hi-Lin Wu, Long-Sun Ro, Shih-Ming Jung, Tzung-Chang Tsai, Chun-Che Chu, Rong-Kuo Lyu, Chin-Chang Huang, Hung-Chou Kuo*
Clinical and Genetic Analysis of Taiwanese Patients with Hereditary Spastic Paraplegia Type 5 Eur J Neurol 2014. doi:10.1111/ene.12407. Min-Yu Lan, Tu-Hseuh Yeh, Yung-Yee Chang, Hung-Chou Kuo, H Sunny Sun, Szu-Chia Lai, Chin-Song Lu
Motor Conduction Findings in Fisher Syndrome Eur Neurol 2013;70:276-280. (SCI) Rong-Kuo Lyu, Chun-Che Chu, Hung-Chou Kuo, Kuo-Hsuan Chang, Long-Sun Ro
Distinct features between longitudinally extensive transverse myelitis presenting with and without anti-aquaporin 4 antibodies Mult Scler. 2013;19:299-307. Chang KH, Lyu RK, Chen CM, Wu YR, Chang HS, Huang CC, Kuo HC, Chu CC, Hsu WC, Ro LS
Regional Amyloid Deposition in Amnestic Mild Cognitive Impairment and Alzheimer's Disease Evaluated by [18F]AV-45 Positron Emission Tomography in Chinese Population PLoS ONE 2013; 8: e58974. Kuo-Lun Huang, Kun-Ju Lin, Ing-Tsung Hsiou, Hung-Chou Kuo, Wen-Chuin Hsu, Wen-Li Chuang, Mei-Ping Kung, Shiaw-Pyng Wey, Chia-Ju Hsieh, Yau-Yau Wei, Yzu-Chen Yen, Ching-Chang Huang
Sensory Conduction Study in Fisher Syndrome: Patterns of Abnormalities and Their Clinical Correlation Eur Neurol 2013; 70:27-32. Rong-Kuo Lyu, Kuo-Hsuan Chang, Chun-Che Chu, Hung-Chou Kuo, Long-Sun Ro
Brain fluorodeoxyglucose positron emission tomography( 18 FDG PET) in patients with acute thallium intoxication Clin Toxicol 2013; 51, 167–173. Liu CH, Lin KJ, Wang HM , Kuo HC , Chuang WL, Weng YH, Shih TS, Huang CC
Use of a Modified Spatial-Context Memory Test to Detect Amnestic Mild Cognitive Impairment PLoS ONE. 2013; 8(2): e57030. (SCI) Hsuan-Min Wang, Chien-Ming Yang, Wan-Chin Kuo, Chin-Chang Huang, Hung-Chou Kuo*
Analyses of haptoglobin level in the cerebrospinal fluid and serum of patients with neuromyelitis optica and multiple sclerosis Clinica Chimica Acta. 2013; 417:26-30. Kuo-Hsuan Chang, Mu-Yun Tseng, Long-Sun Ro, Rong-Kuo Lyu, Yu-Han Tai, Hong-Shiu Chang, Yih-Ru Wu, Chin-Chang Huang, Wen-Chuin Hsu, Hung-Chou Kuo, Chun-Che Chu, Chiung-Mei Chen
Association between GRN rs5848 polymorphism and Parkinson's disease in Taiwanese population PLoS ONE. 2013; 8(1): e54448. Kuo-Hsuan Chang, Chiung-Mei Chen, Yi-Chun Chen, Ya-Chin Hsiao, Chin-Chang Huang, Hung-Chou Kuo, Hsuan-Chu Hsu, Guey-Jen Lee-Chen,, Yih-Ru Wu
Long-term follow-up of spinal and bulbar muscular atrophy in Taiwan J Formos Med Assoc. 2013;112 (6):326-31. Ser-Chen Fu, Hung-Chou Kuo, Chun-Che Chu, Yih-Ru Wu, Long-Sun Ro, Chin-San Liu, Chin-Chang Huang
Frequency of the C9orf72 hexanucleotide repeat expansion in patients with amyotrophic lateral sclerosis and frontotemporal dementia: a cross-sectional study Lancet Neurol 2012; 11: 323-30. Elisa Majounie, Alan E Renton, Kin Mok, Elise G P Dopper, Adrian Waite, Sara Rollinson, Adriano Chio, Gabriella Restagno, Nayia Nicolaou, Javier Simon-Sanchez, John C van Swieten, Yevgeniya Abramzon, Janel O Johnson, Michael Sendtner, Roger Pamphlett, Richard W Orrell, Simon Mead, Katie C Sidle, Henry Houlden, Jonathan D Rohrer, Karen E Morrison, Hardev Pall, Kevin Talbot, Olaf Ansorge, The Chromosome 9-ALS/FTD Consortium(…Hung-Chou Kuo)
Features of varicella zoster virus myelitis and dependence on immune status J Neurol Sci. 2012; 318:19-24. Chih-Hsien Hung, Kuo-Hsuan Chang, Hung-Chou Kuo, Chin-Chang Huang, Ming-Feng Liao, Yu-Tai Tsai, Long-Sun Ro